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HuntingtinPolyclonalAntibody
CatalogNo.:AB0080-200
Price/Unit:EUR320.00
Source:Goat
Quantity/unitsize:600µg
Description:HuntingtinisaproteinlinkedtoHuntington"sdisease,aneurodegenerativedisordercharacterizedbylossofstriatalneurons.Alternativenames:HD,HTTandIT15antibody.
Form:Polyclonalantibodysuppliedasa200µl(3mg/ml)aliquotinPBS,20%glyceroland0.05%sodiumazide.Thisantibodyisepitope-affinitypurifiedfromgoatantiserum.
Immunogen:Purifiedrecombinantpeptidederivedfromwithinresidues85to200aaofhumanHTTproducedinE.coli.
Specificity:Reactshuntingtinprotein,aminoacids85-200.Theantibodyrecognizeswildtypeandmutanthuntingtin.
Reactivity:Reactsagainsthuman,ratandmouseproteins.
Usage:Westernblot 1:500-1:2,000Immunofluorescence 1:500-1:2,000Immunohistochemistry(paraffin) 1:500-1:2,000Immunohistochemistry(frozen) 1:500-1:2,000
Reactivitychart
| Sample | WesternBlot | Immuno-fluorescence | Immuno-Histochemistry(p) | Immuno-Histochemistry(f) | human | +++ | +++ | +++ | +++ | rat | +++ | +++ | +++ | +++ | mouse | +++ | +++ | +++ | +++ | canine | +++ | +++ | +++ | +++ | monkey | +++ | +++ | +++ | +++ |
|---|
Storage:Storeat-20Cforlongtermstorage.Storeat2-8Cforuptoonemonth.
Specialinstructions:Avoidfreeze/thawcycles.

References
1.MiniarikovaJ,ZimmerV,MartierR,etal.GeneTher.2017Oct.PMID:287712342.MeunierC,MerienneN,JolléC,etal.Glia.2016Jul21.PMID:274424863.DéglonN,MerienneN,Genomeeditingforthetreatmentofhuntington"sdisease,EP2982758A1Patent,2014Forresearchuseonly,notfordiagnosticuse
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