IBL/Titin N片段ELISA/30124254/

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货号:30124254
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品牌:IBL
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Kitsize12x8
MethodELISA
Incubationtime1x1h,2x30min.
Standardrange46.00-3000pmol/L
Specimen/Volumes20µLurine
Substrate/isotopeTMB450nm
RegulatoryStatus:Forresearchuseonly
Detailsfor: TitinN-FragmentELISA
Originalarticle#27900
Titin(connectin)isaproteinthatconsistsof34,350amino-acidsandspecificallyexpressesincross-striatedmuscle.Themolecularweightofhumantitinis3,816kDaanditisconsideredthelargestproteinamongallknownproteinsinalivingbody.Itisasarcomerestructuredproteinthatisaminimumunitofmyofibrillaryproteinandithasaroleasanelasticproteinforrecoveringthelengthofshortenedsarcomeresbyitscontraction.Ithasbeenknownthattitiniscleavedbymetabolicenzymessuchascalpainandmatrixmetalloproteaseifmusclesaredamaged.Infact,ithasbeenconfirmedthattitinisdramaticallycleavedinskeletalmusclesofmusculardystrophypatientsandvarioustitinfragmentsareconfirmedinbloodandurine.IthasbeenreportedthattheNfragment(26kDa)andtheCfragment(12kDa)areespeciallyincreasedinurineofmusculardystrophypatientsanditisalsosuggestedthatitcanbeacandidateasanon-invasivenessbioMarkerformonitoringstatusofmuscles.
ThisELISAkitcanmeasuretitinNfragmentinhumanandraturine.

Separatecontrolsetavailableonrequest
ForconcretedatapleaseconsulttheInstructionforUseinthedownloadboxontherightside.
iBL的Tecan由四名工程师于1980年在瑞士Hombrechtikon村成立,旨在开发测量,分析和实验室自动化设备。最初的办公室位于经过翻新的农舍中,这是首席执行官兼创始人亨氏·阿普兰纳普(Heinz Abplanalp)的家庭住宅。